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HTT

HTT,全稱為亨廷頓蛋白,是一種廣泛表達(dá)于人體各器官的蛋白質(zhì),尤其在腦部中起重要作用。該蛋白的正常功能尚未完全明確,但研究表明其可能參與神經(jīng)系統(tǒng)發(fā)育、細(xì)胞內(nèi)吞和分泌以及抑制細(xì)胞凋亡等過(guò)程。HTT蛋白的異常變異會(huì)導(dǎo)致亨廷頓舞蹈癥,這是一種遺傳性神經(jīng)退行性疾病,其特征是機(jī)體運(yùn)動(dòng)和認(rèn)知功能的進(jìn)行性障礙或紊亂。亨廷頓舞蹈癥由HTT基因第一個(gè)外顯子CAG序列的重復(fù)擴(kuò)增引起,導(dǎo)致亨廷頓蛋白的多聚谷氨酰胺束延長(zhǎng),從而引發(fā)蛋白質(zhì)聚集和神經(jīng)變性。
針對(duì)亨廷頓舞蹈癥的藥物研發(fā)主要集中在抑制HTT蛋白的聚集和改善神經(jīng)元功能等方面,例如輝大基因開(kāi)發(fā)的基于Cas12Max的基因編輯療法,旨在降低HTT蛋白的表達(dá)水平,從而緩解疾病癥狀。此外,抗亨廷頓蛋白抗體和RNA干擾技術(shù)也被探索用于治療亨廷頓舞蹈癥。盡管目前尚無(wú)根治方法,但這些研究進(jìn)展為未來(lái)治療提供了新的希望。

熱銷產(chǎn)品

HTT Recombinant Monoclonal Antibody (CSB-RA802195A0HU)

驗(yàn)證數(shù)據(jù)

CSB-RA802195A0HU

IHC image of CSB-RA802195A0HU diluted at 1:100 and staining in paraffin-embedded human small intestine tissue performed on a Leica BondTM system. After dewaxing and hydration, antigen retrieval was mediated by high pressure in a citrate buffer (pH 6.0). Section was blocked with 10% normal goat serum 30min at RT. Then primary antibody (1% BSA) was incubated at 4℃ overnight. The primary is detected by a Goat anti-rabbit IgG polymer labeled by HRP and visualized using 0.05% DAB.

CSB-RA802195A0HU

IHC image of CSB-RA802195A0HU diluted at 1:100 and staining in paraffin-embedded human brain tissue performed on a Leica BondTM system. After dewaxing and hydration, antigen retrieval was mediated by high pressure in a citrate buffer (pH 6.0). Section was blocked with 10% normal goat serum 30min at RT. Then primary antibody (1% BSA) was incubated at 4℃ overnight. The primary is detected by a Goat anti-rabbit IgG polymer labeled by HRP and visualized using 0.05% DAB.

Human Huntingtin(HTT) ELISA kit (CSB-EL010905HU)

驗(yàn)證數(shù)據(jù)

CSB-EL010905HU 標(biāo)準(zhǔn)曲線

貨號(hào):CSB-EL010905HU

規(guī)格:96T/48T

靈敏度:3.125 pg/mL

檢測(cè)范圍:12.5 pg/mL-800 pg/mL

These standard curves are provided for demonstration only. A standard curve should be generated for each set of samples assayed.

HTT Antibodies

HTT for Homo sapiens (Human)

HTT Proteins

HTT Proteins for Homo sapiens (Human)

HTT ELISA Kit

HTT ELISA Kit for Homo sapiens (Human)